martes, 4 de diciembre de 2012

Anomalías craneofaciales

Manejo de la vía aérea para neonatos con onfalocele occipital; revisión de 17 casos


Airway management for occipital encephalocele in neonatal patients: A review of 17 cases.
Yιldιrιm ZB, Avci E, Torun F, Cengiz M, Cigdem A, Karabağ H, Karaman H.
Department of Anesthesiology and Reanimation, Dicle University, Diyarbakir, Turkey.
J Neurosci Rural Pract. 2011 Jul;2(2):159-61.
Abstract
INTRODUCTION: Encephalocele, midline defect of cranial bone fusion, occurs most frequently in the occipital region. Airway management in pediatric patients with craniofacial disorders poses many challenges to the anesthesiologist. The purpose of this study is to describe the airway problems encountered for such cases, and describe how these problems were managed. MATERIALS AND METHODS: We reviewed the charts of occipital encephalocele newborn that were treated by surgical correction in Harran University Hospital during 2006-2008. The collected data were categorized into preoperative, intraoperative, and postoperative data.
RESULTS: The mean age of the patients was 5.17 days. Of these 17 patients, eight patients (47.1%) had hydrocephaly, one patient (5.8%) with Dandy Walker syndrome. Micrognathia, macroglossia, restriction in neck movements were recorded as the reasons in six cases each. No major anesthetic complication was found. CONCLUSIONS: We reported perioperative management in 17 occipital encephalocele infant. Comprehensive care during peroperative period is essential for successful outcome.
http://www.ncbi.nlm.nih.gov/pmc/articles/PMC3159353/


ANOMALÍAS CRANEOFACIALES
DR. JUAN PABLO SOROLLA P.
REV. MED. CLIN. CONDES - 2010; 21(1) 5 - 15
RESUMEN
Las malformaciones craneofaciales son algunas de las patolo¬gías más prevalentes en la edad pediátrica. Podemos distin¬guir dos grandes grupos: las producidas por un cierre precoz de las suturas del esqueleto craneofacial, las craneosinosto¬sis y faciocraneosinostosis; y las que actualmente se pueden considerar neurocrestopatías, como los síndromes de primer y segundo arcos branquiales y las fisuras orofaciales como la fisura labiopalatina.
Se describen las principales características de los síndromes más frecuentes y los tratamientos, desde los más empleados a los más innovadores, como las técnicas endoscópicas y las de distracción ósea.
Palabras clave: Malformaciones craneofaciales, craneosinos¬tosis, faciocraneosinostosis, neurocristopatías, tratamiento quirúrgico.
http://www.clinicalascondes.com/area-academica/pdf/MED_21_1/001_anomalias_craneofaciales.pdf



Atentamente
Dr. Enrique Hernandez-Cortez
Anestesiología y Medicina del Dolor
www.anestesia-dolor.org

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